First to describe progressive bulbar paralysis.

It causes progressive bulbar paralysis due to involvement of motor neurons of the cranial nerve nuclei.

The most frequent symptoms at onset of progressive bulbar paralysis of childhood has been a unilateral facial paralysis.

Differential diagnosis of BVVL includes Boltshauser syndrome, Madras disease, progressive bulbar paralysis of Fazio Londe, Nathalie syndrome and ALS (Nair 2006)