Bronchopulmonary sequestration (BPS) is a rare congenital malformation of the lower respiratory tract.

Congenital cystic adenomatoid malformation (CCAM) is a congenital disorder of the lung similar to bronchopulmonary sequestration.

Causes of airway compression in newborn babies result from a number of rare congenital disorders, including bronchopulmonary sequestration, congenital cystic adenomatoid malformation, mouth or neck tumor such as teratoma, and lung or pleural tumor such as pleuropulmonary blastoma.

A pulmonary sequestration (also known as a bronchopulmonary sequestration or cystic lung lesion), is a medical condition wherein a piece of tissue that ultimately develops into lung tissue is not attached to the pulmonary arterial blood supply, as is the case in normally developing lung.