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Triple-A syndrome (AAA), also known as Achalasia-Addisonianism-Alacrimia syndrome or Allgrove syndrome, is a rare autosomal recessive congenital disorder.
Triple-A syndrome is associated with mutations in the AAAS gene, which encodes a protein known as ALADIN (ALacrima Achalasia aDrenal Insuffiency Neurologic disorder).
Triple A stands for achalasia-addisonianism-alacrima syndrome.